102636-82-8
中文名稱
GLUTARYLCARNITINE
英文名稱
Glutaroyl carnitine
CAS
102636-82-8
分子式
C12H21NO6
MOL 文件
102636-82-8.mol
102636-82-8 結(jié)構(gòu)式
基本信息
中文別名
戊二?；鈮A 英文別名
Glutaroyl carnitineDL-Glutaryl Carnitine
(L)-Glutaryl Carnitine
Glutaroyl N-(methyl-D3)-carnitine
L-Glutaryl Carnitine DISCONTINUED. Please see G597605
(2R)-3-Carboxy-2-(4-carboxy-1-oxobutoxy)-N,N,N-triMethyl-1-propanaMiniuM Inner Salt
物理化學(xué)性質(zhì)
儲存條件2-8°C
溶解度可溶于二甲基亞砜、甲醇、水
形態(tài)Gel
顏色透明無色
旋光性 (optical activity)[α]/D -20±2°, c = 1 in H2O
穩(wěn)定性非常吸濕
常見問題列表
生物活性
Glutarylcarnitine 丙二酸尿癥和 I 型戊二酸尿癥的重要診斷代謝物。靶點(diǎn)
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Human Endogenous Metabolite
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體外研究
Malonylcarnitine and Glutarylcarnitine are important diagnostic metabolites in the screening of dried blood spots by tandem mass spectrometry.
The urinary excretion of glutarylcarnitine is a specific biochemical marker of glutaric acidemia type I (GA-1). The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I.